Purpose : Forward pulmonary blood flow may be absent in some neonates with Ebstein's anomaly by anatomical or functional pulmonary atresia in association with the elevated pulmonary vascular resistance, patent ductus arteriosus and tricuspid regurgitation. We reviewed the presentation and outcomes of symptomatic neonates with Ebstein's anomaly focusing on the pulmonary atresia. Methods : Clinical presentation and outcome of 15 symptomatic... |
Pediatricians often encounter some electrocardiographic abnormalities in infants and children. However, treatment or referral to pediatric cardiologist is not indicated for all arrhythmias. Many of them are benign in nature. Benign arrhythmias can be defined as the arrhythmias that no serious problem currently exists and no treatment is needed. The prognosis of benign arrhythmias is so good that the condition... |
Purpose : We intended to find out the role of transesophageal atrial pacing in evaluation of infants and children with palpitation of unknown origin. Methods : We tried transesophageal atrial pacing study in 69 infants and children with palpitation, in whom tachycardia wasn't documented in electrocardiogram and reviewed retrospectively the records of transesophageal pacing and medical records of theses patients to... |
Purpose : The purpose of this study is to examine the usefulness of the head-up tilt test for diagnosis of unexplained syncope in children. Methods : Head-up tilt test results and clinical features of 41 children with unexplained syncope, presyncope, dizziness and seizure were studied from January, 1997 through January, 2001 at Asan Medical Center. Medical records of children were reviewed retrospectively. The children... |
Purpose : Anthracycline induced cardiotoxicity is well known and its pathology is characterized by localized myocardial cell necrosis and myocardial fibrosis. The variability in QT interval duration amongst the different leads of the standard 12-lead ECG(QT dispersion) is considered to reflect inhomogenous repolarization of the myocardium. The aim of this study was to assess the effects of anthracycline on cardiac... |
Purpose : The purpose of this study was to evaluate the hemodynamic effect of transposition of the great arteries(TGA) on neuro-development by measuring the cerebral metabolites before and 1 year after open heart surgery(OHS) by localized in vivo 1H-magnetic resonance spectroscopy(1H- MRS) along with Bayley scales of infants development II(BSID II). Methods : Full-term newborns(N=13) with TGA and intact ventricular septum... |
Purpose : Malnutrition and failure to thrive have long been recognized as common systemic consequences of congenital heart disease(CHD). But there is little data about the prevalence and severity of malnutrition with CHD in Korea. We designed this study to determine the prevalence of malnutrition among hospitalized children with CHD. Methods : We reviewed 100 hospitalized children with CHD who were... |
Purpose : Histologic studies have revealed ectopic location and hypoplasia of sinus nodal tissue in left atrial isomerism. The purpose of this study is to characterize the atrial rhythms corresponding to these histologic abnormalities in left atrial isomerism. Electrocardiograms in left atrial isomerism are characterized by multiple atrial rhythms with abnormal P-wave axes, but the complex nature of atrial rhythms... |
Purpose : The aim of this study was to assess the involvement of several organs patients with Marfan syndrome in Korea. Also the clinical features in childhood patients with Marfan syndrome were assessed. Methods : Thirty-eight cases of Marfan syndrome were enrolled in this study. Clinical evaluations of the musculoskeletal, cardiovascular and occular system were performed in all cases. Results : The... |
Purpose : Although the data of radiofrequency catheter ablation(RFCA) of supraventricular tachycardia in adults has been accumulated in several centers in Korea, few data are available on its efficacy and safety in pediatric ages. We reviewed the data in young patients who underwent this procedure in a pediatric cardiology center, to evaluate the indications, early results, complications, and short-term follow-up data. Methods : We retrospectively... |
Pulmonary artery sling with bridging bronchus is not only rare but also difficult to diagnose unless specially sought. When young infant suffers from prolonged or recurrent wheezing, possibility of underlying anomalies of the tracheobronchial trees or great vessels should be considered, even though bronchiolitis and gastroesophageal reflux are the most common causes. We experienced four cases of pulmonary artery sling with... |
Atrial flutter is a potentially life threatening complication of repair or palliation of congenital heart disease and is frequently drug resistant. Recent studies in human have demonstrated that common type atrial flutter is due to macro-reentry in the right atrium and that the reentrant circuit may involve slow conduction in the low posteroseptal area of the right atrium. Catheter ablation of atrial flutter has... |
Atrial flutter is an infrequent, but potentially unstable tachyarrythmia that occurs in pediatric ages. Transesophageal atrial pacing was used for treatment of 10 episodes of atrial flutter in 7 patients. At the time of atrial flutter conversion, patients were 6 days to 14 years old. 6 patients had associated with congenital heart disease. The atrial cycle length of atrial flutter ranged from... |
The scimitar syndrome, a rare complex anomaly, consists essentially of an anomalous pulmonary vein draining whole or part of right lung into inferior vena cava and its curved Turkish sword (scimitar) like appearance has provided the name of this syndrome. Associated anomalies are frequent, such as hypoplasia of the right lung and right pulmonary artery, abnormalities of bronchial architecture and lobation, rightward displacement of... |
During the period of 2 years, between January 1986 and December 1987, 36 patients, aged 2 years to 18 years, with congenital pulmonary valve stenosis(PVS) (with peak systolic transvalvar gradient over 30 mmHg) underwent percutaneous transluminal balloon valvuloplasty(TBV) at Sejong General Hospital m Korea. Of a group of 36 patients, 26 were treated successfully by the conventional balloon valve dilatation technique, and 6 were treated... |
Kasabach-Merritt Syndrome is association of thrombocytopenia with giant hemangioma. A 20 days, male patient had thrombocytopenia, the hemangioma involved the skin of the right distal femur. This patient was placed on combined therapy with radiation and steroid. Following the conservative therapy, the hemangioma regressed and the platelet returned to normal range. We presented the case with brief review of the literatures. |
Ninety-nine cases of ventricular septal defect with septal aneurysm which were confirmed by angiocardiography and 2-D echocardiography during the period of 2 years from 1983 to 1984 at SNUH were studied and analyzed. The summary of the findings are as follows: 1) Septal aneurysm was found in 99(26.9%) of 368 cases of total VSD and in 38.2% among membranous VSD.... |
It is well known that chronic anemia is associated with hemodynamic alterations like increased cardiac output and stroke volume and decreased peripheral vascular resistance. Left ventricular size and function were studied by echocardiography in 16 chronic anemia patients, mainly aplastic anemia, without evidence of cardiac decompensation. Left ventricular dimension, stroke volume, ejection fraction and fractional shortening were calculated. The LV... |